Definition of Branched Chain Ketoaciduria in English :
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Branched Chain Ketoaciduria meaning in English
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Branched Chain Ketoaciduria
see synonyms of branched chain ketoaciduriaNoun
1. branched chain ketoaciduria, maple syrup urine disease
an inherited disorder of metabolism in which the urine has a odor characteristic of maple syrup; if untreated it can lead to mental retardation and death in early childhood
WordNet Lexical Database for English. Princeton University. 2010.