Definition of Branched Chain Ketoaciduria in English :

Define Branched Chain Ketoaciduria in English

Branched Chain Ketoaciduria meaning in English

Meaning of Branched Chain Ketoaciduria in English

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Branched Chain Ketoaciduria pronunciation in English

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Branched Chain Ketoaciduria

see synonyms of branched chain ketoaciduria

Noun

1. branched chain ketoaciduria, maple syrup urine disease

an inherited disorder of metabolism in which the urine has a odor characteristic of maple syrup; if untreated it can lead to mental retardation and death in early childhood

WordNet Lexical Database for English. Princeton University. 2010.